Chapter 6

Food For Phenylketonuric Consumers

Elevina Pérez Sira* and Antonieta Mahfoud

Abstract

Phenylketonuria (PKU) is an inborn error of amino acid metabolism, characterized by persistent hyperphenylalaninemia. There is no cure for PKU, however, early diagnosis and treatment during the first month of life, make it possible to prevent all the mentioned consequences. The treatment of classic and moderate PKU is nutritional, based on a diet restricted in Phe, and supplemented with special formulas free of Phe. The chapter is handling phenylketonuria (PKU) overview, highflying the treatment strategies, incidence, nutrition, and PKU Diet, and development and innovation of food for PKU including some home recipes.

Total Pages: 152-172 (21)

Purchase Chapter  Book Details